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Transarterial coil embolization of an aortic root pseudoaneurym in a patient with Loeys-Dietz syndrome: a case report D’Ortenzio, Robert; Cardarelli-Leite, Leandro; Dhatt, Ravjot; Saw, Jacqueline; Heran, Manraj

Abstract

Background: Loeys-Dietz syndrome (LDS) is a rare autosomal-dominant connective tissue disorder characterized by arterial aneurysms and vascular friability. Surgical intervention for LDS patients carries significant morbidity and mortality. Currently, the standard management of aortic root pseudoaneurysms is surgical intervention. Case presentation: A 20 year old male with LDS presented with a progressively enlarging ascending aortic aneurysm. He underwent a Bentall-type aortic root replacement complicated by a 20 mm aortic root anastomotic pseudoaneurysm. Due to the patient’s high risk for repeat surgical intervention, he underwent successful transarterial coil embolization of his aortic root pseudoaneurysm without complication. Conclusions: Coil embolization may provide an alternative treatment for patients presenting with aortic root pseudoaneurysm who are high risk for traditional surgical treatment, such as those with connective tissue disease.

Item Metadata

Title
Transarterial coil embolization of an aortic root pseudoaneurym in a patient with Loeys-Dietz syndrome: a case report
Creator
D’Ortenzio, Robert; Cardarelli-Leite, Leandro; Dhatt, Ravjot; Saw, Jacqueline; Heran, Manraj
Contributor
Children's Hospital (Vancouver, B.C.)
Publisher
Springer International Publishing
Date Issued
2020-12-08
Description
Background: Loeys-Dietz syndrome (LDS) is a rare autosomal-dominant connective tissue disorder characterized by arterial aneurysms and vascular friability. Surgical intervention for LDS patients carries significant morbidity and mortality. Currently, the standard management of aortic root pseudoaneurysms is surgical intervention. Case presentation: A 20 year old male with LDS presented with a progressively enlarging ascending aortic aneurysm. He underwent a Bentall-type aortic root replacement complicated by a 20 mm aortic root anastomotic pseudoaneurysm. Due to the patient’s high risk for repeat surgical intervention, he underwent successful transarterial coil embolization of his aortic root pseudoaneurysm without complication. Conclusions: Coil embolization may provide an alternative treatment for patients presenting with aortic root pseudoaneurysm who are high risk for traditional surgical treatment, such as those with connective tissue disease.
Subject
Aortic aneurysm; Aortic pseudoaneurysm; Bentall; Interventional procedures; Loeys-Dietz; Connective tissue disease; Coil embolization; Cardiology
Genre
Article
Type
Text
Language
eng
Date Available
2020-12-16
Provider
Vancouver : University of British Columbia Library
Rights
Attribution 4.0 International (CC BY 4.0)
DOI
10.14288/1.0395319
URI
http://hdl.handle.net/2429/76819
Affiliation
Medicine, Faculty of; Other UBC; Non UBC; Medicine, Department of; Radiology, Department of
Citation
CVIR Endovascular. 2020 Dec 08;3(1):94
Publisher DOI
10.1186/s42155-020-00184-5
Peer Review Status
Reviewed
Scholarly Level
Faculty
Copyright Holder
The Author(s)
Rights URI
http://creativecommons.org/licenses/by/4.0/
Aggregated Source Repository
DSpace

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Rights

Attribution 4.0 International (CC BY 4.0)